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Osler-Rendu-Weber Disease
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Telangiectasias in the oral cavity, in the palate.
Osler-Rendu-Weber disease, also called Hereditary hemorrhagic telangiectasia, is a vascular disorder resulting from a vascular development abnormality. The disease has an autosomal dominant transmission, so these patients usually have a characteristic family history. The venules and capillaries in the skin and mucous membranes are dilatated and convoluted, and bleeding can be spontaneous or a result of a minor trauma.
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Gastric telangiectasias
The lesions are about 3 millimeters in diameter and can be seen in the nasal mucous membranes, lips, gingiva, palate. There may also be telangiectasias in the skin on the face, trunk and hands. Visceral telangiectasias can be found in the gastrointestinal tract and also in the lungs and genitourinary region. The liver is involved in about 1/3 of the patients, but the liver involvment rarely causes any serious trouble.
Telangiectasias can also be found in the brain, and cerebral hamorrhage due to this disease has been reported.
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